How rare is Long QT Syndrome?

Long QT Syndrome is considered a rare disease as according to literature it affects around 1-2000 people. Long QT syndrome is usually inherited in an autosomal dominant manner. This means that a child has a 50% chance of inheriting the condition if one parent carries the gene mutation responsible for Long QT . There are also autosomal recessive forms, where a child must inherit the gene mutation from both parents to develop the condition (Jervell and Lange-Nielsen syndrome).